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Initial acquisition and succession of the cystic fibrosis lung microbiome is associated with disease progression in infants and preschool children

Assessment of p.Phe508del-CFTR functional restoration in pediatric primary cystic fibrosis airway epithelial cells Abstract Background Mutations in

The potential of antisense oligonucleotide therapies for inherited childhood lung diseases Antisense oligonucleotides (AOs) are an emerging

Clinical utility of surveillance computed tomography scans in infants with cystic fibrosis Abstract Background: In cystic fibrosis (CF), irreversible

Hypoxia and sterile inflammation in cystic fibrosis airways mechanisms and potential therapies ABSTRACT Cystic fibrosis is one of the most common

Lack of small colony variants of Staphylococcus aureus from lower respiratory tract specimens Abstract Background: Small-colony variants (SCVs) of

Sialic acid-to-urea ratio as a measure of airway surface hydration. Although airway mucus dehydration is key to pathophysiology of cystic fibrosis (CF

Multiple Breath Washout Cannot Be Used for Tidal Breath Parameter Analysis in Infants Background: Multiple breath washout (MBW) testing with SF6 gas

Lung inflammation and simulated airway resistance in infants with cystic fibrosis Cystic fibrosis (CF) is characterized by small airway disease; but

Update on SLC6A14 in lung and gastrointestinal physiology and physiopathology: focus on cystic fibrosis The solute carrier family 6 member 14 (